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KMID : 0358320130540030209
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Korean Journal of Urology
2013 Volume.54 No. 3 p.209 ~ p.211
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Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
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Kim Sun-Chan
Kim Tae-Gu
Choi Seung-Kwon
Kim Myung-Joon
Min Gyeong-Eun
Lee Hyung-Lae
Yoo Koo-Han
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Abstract
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Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
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KEYWORD
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Immunoglobulin G, Sclerosis, Ureter
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